[Anesthesia in a child operated for cleft lip associated with Patau's syndrome].
نویسندگان
چکیده
Patients with Patau's syndrome (Trisomy 13) have multiple craniofacial, cardiac, neurological and renal anomalies with very less life expectancy. Among craniofacial anomalies cleft lip and palate are common. These craniofacial and cardiac anomalies present difficulties with anesthesia. We therefore describe the anesthetic management in the case of a Trisomy 13 child for operated for cleft lip at 10 months of age.
منابع مشابه
Roberts-SC syndrome, a rare syndrome and cleft palate repair
Roberts SC syndrome is a rare syndrome with only 17 previously recognized patients reported in medical literature. The syndrome is characterized by multiple malformations, particularly, symmetrical limb reduction, craniofacial anomalies such as bilateral cleft lip and palate, micrognathia, and severe growth and mental retardation. Our patient, a young child of five years having Roberts-SC, was ...
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ورودعنوان ژورنال:
- Revista brasileira de anestesiologia
دوره 68 2 شماره
صفحات -
تاریخ انتشار 2018